Taussig–Bing syndrome: Difference between revisions
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'''Taussig–Bing syndrome''' (after [[Helen B. Taussig]] and [[Richard Bing]]) is a [[cyanotic heart defect|cyanotic]] [[congenital]] [[congenital heart defect|heart defect]]<ref>{{Cite journal|last=Konstantinov|first=Igor E.|date=2009|title=Taussig-Bing Anomaly|url=http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2801930/|journal=Texas Heart Institute Journal|volume=36|issue=6|pages=580–585|issn=0730-2347|pmc=2801930|pmid=20069085}}</ref> in which the patient has both [[double outlet right ventricle]] ('''DORV''') and [[subpulmonic]] [[ventricular septal defect]] ('''VSD'''). |
'''Taussig–Bing syndrome''' (after [[Helen B. Taussig]] and [[Richard Bing]]) is a [[cyanotic heart defect|cyanotic]] [[congenital]] [[congenital heart defect|heart defect]]<ref>{{Cite journal|last=Konstantinov|first=Igor E.|date=2009|title=Taussig-Bing Anomaly|url=http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2801930/|journal=Texas Heart Institute Journal|volume=36|issue=6|pages=580–585|issn=0730-2347|pmc=2801930|pmid=20069085}}</ref> in which the patient has both [[double outlet right ventricle]] ('''DORV''') and [[subpulmonic]] [[ventricular septal defect]] ('''VSD''').<ref>{{cite book|last1=Ramrakha|first1=Punit S.|last2=Ramrakha|first2=Punit|last3=Hill|first3=Jonathan|title=Oxford Handbook of Cardiology|date=2012|publisher=OUP Oxford|isbn=9780199643219|page=707|accessdate=31 October 2017|language=en}}</ref> |
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In DORV, instead of the normal situation where blood from the [[left ventricle]] ('''LV''') flows out to the [[aorta]] and blood from the [[right ventricle]] ('''RV''') flows out to the [[pulmonary artery]], both [[aorta]] and [[pulmonary artery]] are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is [[subpulmonic]] (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta. |
In DORV, instead of the normal situation where blood from the [[left ventricle]] ('''LV''') flows out to the [[aorta]] and blood from the [[right ventricle]] ('''RV''') flows out to the [[pulmonary artery]], both [[aorta]] and [[pulmonary artery]] are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is [[subpulmonic]] (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta. |
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Revision as of 11:03, 31 October 2017
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| Taussig–Bing syndrome | |
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| Specialty | Medical genetics  |
Taussig–Bing syndrome (after Helen B. Taussig and Richard Bing) is a cyanotic congenital heart defect[1] in which the patient has both double outlet right ventricle (DORV) and subpulmonic ventricular septal defect (VSD).[2]
In DORV, instead of the normal situation where blood from the left ventricle (LV) flows out to the aorta and blood from the right ventricle (RV) flows out to the pulmonary artery, both aorta and pulmonary artery are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is subpulmonic (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta.
The clinical manifestations of a Taussig-Bing anomaly, therefore, are much like those of dextro-Transposition of the great arteries (but the surgical repair is different). It can be corrected surgically also with the arterial switch operation (ASO).
It is managed with Rastelli procedure.
References
- ^ Konstantinov, Igor E. (2009). "Taussig-Bing Anomaly". Texas Heart Institute Journal. 36 (6): 580–585. ISSN 0730-2347. PMC 2801930. PMID 20069085.
- ^ Ramrakha, Punit S.; Ramrakha, Punit; Hill, Jonathan (2012). Oxford Handbook of Cardiology. OUP Oxford. p. 707. ISBN 9780199643219.
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